Platelet storage pool deficiency
|Platelet storage pool deficiency|
|Classification and external resources|
Platelet storage pool deficiency is a type of coagulopathy characterized by defects in the granules in platelets, particularly a lack of granular non-metabolic ADP. Patients with ADP deficient "Storage Pool Disease" present a prolonged bleeding time due to impaired aggregation response to fibrillar collagen.
It may involve the alpha granules or the dense granules.
- Dense granules
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